关键词: Afectación linfática Derrame pleural Linfangiectasias Linfedema Lymphangiectasias Lymphatic involvement Lymphedema Pleural effusion Síndrome de las uñas amarillas Yellow nail syndrome

Mesh : Humans Yellow Nail Syndrome / complications Lymph Nodes

来  源:   DOI:10.1016/j.patol.2021.12.003

Abstract:
Yellow nail syndrome is a rare disease of unknown aetiology. Patients with YNS have a characteristic yellowish-coloured nails, pulmonary alterations and primary lymphedema. To the best of our knowledge, only a few reports of autopsy findings in these patients have been published. Its aetiology possibly involves a primary malformation of larger lymph vessels. We describe autopsy findings not previously associated with yellow nail syndrome, such as expansion of mediastinal lymph-nodes and splenic sinusoids. The present autopsy reveals hitherto unreported findings associated with YNS, such as alterations in splenic sinusoids and mediastinal lymph-node sinuses.
摘要:
黄甲综合征是一种病因不明的罕见疾病。患有YNS的患者具有特征性的黄色指甲,肺改变和原发性淋巴水肿。据我们所知,只有少数关于这些患者的尸检结果的报告已经发表.其病因可能涉及较大淋巴管的原发性畸形。我们描述了以前与黄色指甲综合征无关的尸检结果,如纵隔淋巴结和脾窦扩张。目前的尸检揭示了迄今为止未报告的与YNS相关的发现,如脾窦和纵隔淋巴结窦的改变。
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