Mesh : Child Humans Male Arm Arnold-Chiari Malformation / diagnosis diagnostic imaging Edema / etiology Hypesthesia / complications Syringomyelia / complications diagnostic imaging surgery Adult

来  源:   DOI:10.1038/s41394-023-00583-5   PDF(Pubmed)

Abstract:
Chiari malformation type I (CM-I) with cervicothoracic syringomyelia can progress slowly this condition which is very common in clinical practice, particularly in children.
Patients typically present with chronic complaints, including headache, dizziness, and numbness, although are few reports in the literature describing pediatric patients who developed acute neurological deficits caused by CM-I. Here, we report an unusual presentation of this condition; the patient presented with sudden onset arm swelling with no precipitating factors that could explain the diagnosis.
This is an illustrated case report and literature review. The patient\'s condition improved post-operatively; in terms of arm and hand swelling which resolved, but he still complained of persistent numbness on a follow-up visit.
摘要:
背景:Chiari畸形I型(CM-I)伴颈胸脊髓空洞症可以缓慢进展,这种情况在临床实践中非常常见,特别是在儿童中。
方法:患者通常表现为慢性主诉,包括头痛,头晕,麻木,尽管文献中很少有报道描述由CM-I引起的急性神经功能缺损的儿科患者。这里,我们报告了这种情况的异常表现;患者出现突然发作的手臂肿胀,没有可以解释诊断的诱因。
结论:这是一个病例报告和文献综述。患者的病情在术后得到改善;在手臂和手肿胀方面,但他仍然抱怨在后续访问中持续麻木。
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