Abstract:
Apical hypertrophic cardiomyopathy (AHCM) is a relatively rare phenotype of hypertrophic cardiomyopathy, which is characterized by focal thickening of the left ventricular (LV) apical myocardium, showing a spade-shaped shadow on the left ventricle. We present the case of a 59-year-old man who was found to have AHCM, is an asymptomatic orthotopic heart transplantation (HTx) patient. This rare and progressive case of LV apical hypertrophy emerged from the fourth year post surgery. We analyzed the etiology of this case and summarized the clinical manifestations and prognosis of AHCM following HTx by reviewing our case and the literature.
摘要:
心尖肥厚型心肌病(AHCM)是肥厚型心肌病的一种相对罕见的表型,其特征在于左心室(LV)心尖心肌的局灶性增厚,左心室上有铲形的阴影.我们介绍了一个59岁的男子,他被发现患有AHCM,是无症状的原位心脏移植(HTx)患者。这种罕见且进行性的LV根尖肥大病例从手术后第四年出现。我们分析了该病例的病因,并通过复习我们的病例和文献总结了HTx后AHCM的临床表现和预后。