Abstract：
Acute aortic dissection in the paediatric population is rare but lethal. We present two paediatric cases of type A acute aortic dissection that required emergent procedures and were later found to have genetic mutations. High index of suspicion, early clinical diagnosis, prompt treatment, the advantageous collaboration between the paediatric team and aortic surgeons, and familial genetic testing are paramount to achieve a good outcome.
摘要：
儿科人群中的急性主动脉夹层很少见，但致命。我们介绍了两例A型急性主动脉夹层的儿科病例，这些病例需要紧急手术，后来被发现具有基因突变。高度怀疑，早期临床诊断,及时治疗,儿科团队和主动脉外科医生之间的有利合作，家族基因检测对于取得好的结果至关重要。
