Abstract：
Hepatoblastoma is the most common primary malignancy of hepatic origin in children, with an estimated incidence of 0.5-1.5 per million children. Hepatoblastoma classically has an intraparenchymal location, and pedunculated hepatoblastoma is a relatively rare entity. Accurate diagnosis can be challenging due to its extrahepatic location and possibly its thin peduncle, which is not easily identified in imaging.
Here, we report a case of asymptomatic giant palpable hepatoblastoma in the LUQ of a four-month-old male infant, initially suspected of neuroblastoma based on abdominal ultrasound findings. The final diagnosis of giant pedunculated hepatoblastoma was made based on the abdominal CT scan and the diagnosis was confirmed by percutaneous biopsy. Due to the size of the tumor, complete removal of the tumor was not initially possible. Therefore, the patient was treated with several courses of chemotherapy. The tumor was shrunk and then completely removed. The patient was treated, and no complications were found in the 6-month follow-up.
Pedunculated hepatoblastoma is rare but should be considered as a possibility in the case of a perihepatic mass in a pediatric patient that can be confused with other upper abdominal masses such as an adrenal mass. Therefore, in such cases, we must look for the vascular pedicle in the imaging and keep the AFP check in mind.
Here, we report a case of asymptomatic giant palpable hepatoblastoma in the LUQ of a four-month-old male infant, initially suspected of neuroblastoma based on abdominal ultrasound findings. The final diagnosis of giant pedunculated hepatoblastoma was made based on the abdominal CT scan and the diagnosis was confirmed by percutaneous biopsy. Due to the size of the tumor, complete removal of the tumor was not initially possible. Therefore, the patient was treated with several courses of chemotherapy. The tumor was shrunk and then completely removed. The patient was treated, and no complications were found in the 6-month follow-up.
Pedunculated hepatoblastoma is rare but should be considered as a possibility in the case of a perihepatic mass in a pediatric patient that can be confused with other upper abdominal masses such as an adrenal mass. Therefore, in such cases, we must look for the vascular pedicle in the imaging and keep the AFP check in mind.
摘要：
背景：肝母细胞瘤是儿童肝源最常见的原发性恶性肿瘤，估计发病率为每百万儿童0.5-1.5。肝母细胞瘤通常具有实质内位置，带蒂肝母细胞瘤是一种相对罕见的实体。准确的诊断可能是具有挑战性的，因为它的肝外位置和可能的薄花梗，在成像中不容易识别。
方法：这里，我们报告了一个无症状的巨大的可触及的肝母细胞瘤在LUQ的一个4个月大的男婴，最初根据腹部超声检查结果怀疑神经母细胞瘤。根据腹部CT扫描最终诊断为巨大带蒂肝母细胞瘤，并通过经皮穿刺活检证实诊断。由于肿瘤的大小,最初不可能完全切除肿瘤.因此,患者接受了几个疗程的化疗。将肿瘤缩小,然后完全切除。病人接受了治疗,在6个月的随访中没有发现并发症。
结论：未分化的肝母细胞瘤是罕见的，但在儿科患者肝周肿块的情况下，应考虑为可能与其他上腹部肿块如肾上腺肿块混淆。因此,在这种情况下,我们必须在成像中寻找血管蒂，并记住AFP检查。
方法：这里，我们报告了一个无症状的巨大的可触及的肝母细胞瘤在LUQ的一个4个月大的男婴，最初根据腹部超声检查结果怀疑神经母细胞瘤。根据腹部CT扫描最终诊断为巨大带蒂肝母细胞瘤，并通过经皮穿刺活检证实诊断。由于肿瘤的大小,最初不可能完全切除肿瘤.因此,患者接受了几个疗程的化疗。将肿瘤缩小,然后完全切除。病人接受了治疗,在6个月的随访中没有发现并发症。
结论：未分化的肝母细胞瘤是罕见的，但在儿科患者肝周肿块的情况下，应考虑为可能与其他上腹部肿块如肾上腺肿块混淆。因此,在这种情况下,我们必须在成像中寻找血管蒂，并记住AFP检查。
