Abstract：
The patient is a 22-year-old, female. She had a family history of familial adenomatous polyposis(FAP)and a prophylactic total colorectal resection was performed for FAP at age of 18. She presented with fever and abdominal distention and palpated a mass with tenderness in the right lower abdomen. Contrast-enhanced CT scan of the abdomen showed a heterogeneous contrast effect around the tumor margins. With the diagnosis of intra-abdominal desmoid tumor, a partial duodenal resection, small bowel mass resection, and right fallopian tube resection were performed along with the tumor, and an artificial anus was created with the jejunum. Contrast-enhanced CT scan of the abdomen 16 months after resection of desmoid tumor showed a 6.5 cm long desmoid tumor recurrence in the mesentery. She received 5 courses of doxorubicin (DOX)plus dacarbazine(DTIC)therapy followed by continued NSAIDs. Seven years after the operation, she has been able to maintain the shrinkage of the recurrent tumor and is still on medication. Long-term surveillance is necessary because of the possibility of the appearance of other associated lesions in the future.
摘要：
病人22岁,female.她有家族性腺瘤性息肉病（FAP）的家族史，并且在18岁时对FAP进行了预防性全结直肠切除术。她出现发烧和腹胀，并在右下腹部触诊有压痛的肿块。腹部对比增强CT扫描显示肿瘤边缘周围的对比效果不均匀。随着腹内硬纤维瘤的诊断，十二指肠部分切除术,小肠肿块切除术,右输卵管切除术和肿瘤一起进行，用空肠制造了一个人造肛门。硬纤维瘤切除后16个月，腹部增强CT扫描显示肠系膜有6.5厘米长的硬纤维瘤复发。她接受了5个疗程的阿霉素（DOX）加达卡巴嗪（DTIC）治疗，然后继续使用NSAIDs。手术七年后，她已经能够维持复发性肿瘤的缩小，并且仍在服药。由于将来可能出现其他相关病变，因此需要长期监测。
