Abstract：
True hermaphroditism is a rare condition. It is defined as the presence of both testicular and ovarian tissues in the same individual. Sex cord tumour with annular tubules (SCTAT) is a rare stromal tumour of the sex cord that occurs mostly in the ovaries.
A 16-year-old girl presented to the gynaecology department with primary amenorrhea. Gynaecological examination revealed an enlarged clitoris that looked like a small penis. The chromosome karyotype was chimaera. The postoperative pathology confirmed true hermaphroditism with SCTAT. The patient underwent hormonal replacement after an operation and had no evidence of recurrence for 6 months.
Cases of true hermaphroditism with SCTAT are extremely rare conditions. Surgery and hormonal replacement are important for improving the prognosis of such patients.
A 16-year-old girl presented to the gynaecology department with primary amenorrhea. Gynaecological examination revealed an enlarged clitoris that looked like a small penis. The chromosome karyotype was chimaera. The postoperative pathology confirmed true hermaphroditism with SCTAT. The patient underwent hormonal replacement after an operation and had no evidence of recurrence for 6 months.
Cases of true hermaphroditism with SCTAT are extremely rare conditions. Surgery and hormonal replacement are important for improving the prognosis of such patients.
摘要：
背景：真正的两性畸形是一种罕见的疾病。它被定义为睾丸和卵巢组织在同一个人中的存在。具有环状小管的性索肿瘤（SCTAT）是一种罕见的性索间质肿瘤，主要发生在卵巢中。
方法：一名16岁女孩因原发性闭经就诊于妇科。妇科检查显示阴蒂扩大，看起来像一个小阴茎。染色体核型为嵌合体。术后病理证实为SCTAT真两性畸形。该患者在手术后接受了激素替代治疗，并且在6个月内没有复发的证据。
结论：SCTAT的真两性畸形病例极为罕见。手术和激素替代对于改善此类患者的预后很重要。
方法：一名16岁女孩因原发性闭经就诊于妇科。妇科检查显示阴蒂扩大，看起来像一个小阴茎。染色体核型为嵌合体。术后病理证实为SCTAT真两性畸形。该患者在手术后接受了激素替代治疗，并且在6个月内没有复发的证据。
结论：SCTAT的真两性畸形病例极为罕见。手术和激素替代对于改善此类患者的预后很重要。
