%0 Review
%T True hermaphroditism with sex cord tumor with annular tubules (SCTAT): a rare case report and review of the literature.
%A Shi S
%A Tang M
%A Li W
%A Wu H
%A Liu Y
%A Luo Y
%A Ding H
%J BMC Womens Health
%V 22
%N 1
%D 12 2022 27
%M 36575516
%F 2.742
%R 10.1186/s12905-022-02137-7
%X True hermaphroditism is a rare condition. It is defined as the presence of both testicular and ovarian tissues in the same individual. Sex cord tumour with annular tubules (SCTAT) is a rare stromal tumour of the sex cord that occurs mostly in the ovaries.
A 16-year-old girl presented to the gynaecology department with primary amenorrhea. Gynaecological examination revealed an enlarged clitoris that looked like a small penis. The chromosome karyotype was chimaera. The postoperative pathology confirmed true hermaphroditism with SCTAT. The patient underwent hormonal replacement after an operation and had no evidence of recurrence for 6 months.
Cases of true hermaphroditism with SCTAT are extremely rare conditions. Surgery and hormonal replacement are important for improving the prognosis of such patients.