%0 Review %T True hermaphroditism with sex cord tumor with annular tubules (SCTAT): a rare case report and review of the literature. %A Shi S %A Tang M %A Li W %A Wu H %A Liu Y %A Luo Y %A Ding H %J BMC Womens Health %V 22 %N 1 %D 12 2022 27 %M 36575516 %F 2.742 %R 10.1186/s12905-022-02137-7 %X True hermaphroditism is a rare condition. It is defined as the presence of both testicular and ovarian tissues in the same individual. Sex cord tumour with annular tubules (SCTAT) is a rare stromal tumour of the sex cord that occurs mostly in the ovaries.
A 16-year-old girl presented to the gynaecology department with primary amenorrhea. Gynaecological examination revealed an enlarged clitoris that looked like a small penis. The chromosome karyotype was chimaera. The postoperative pathology confirmed true hermaphroditism with SCTAT. The patient underwent hormonal replacement after an operation and had no evidence of recurrence for 6 months.
Cases of true hermaphroditism with SCTAT are extremely rare conditions. Surgery and hormonal replacement are important for improving the prognosis of such patients.