Abstract：
Small intestinal medullary carcinoma (MC) is a newly recognized subclass of small intestinal carcinomas and is an exceptional entity for this site. A search of the literature for similar cases arising in the small intestine revealed only six previously reported cases. Here we present a case of MC arising in the jejunum of a 65-year-old male. The patient presented to the emergency with features of perforation peritonitis with liver metastasis and no known predisposing factors like inflammatory bowel disease and celiac disease. Studies conducted on this tumor\'s colonic counterpart have shown microsatellite instability (MSI) and B-type Raf kinase (BRAF) mutations; however, few exceptions are known. Also, this subtype of carcinoma is known to have a better prognosis than its other histological subtypes.
摘要：
小肠髓样癌（MC）是新认识的小肠癌亚类，是该位点的特殊实体。对小肠中出现的类似病例的文献搜索显示，以前仅报道了6例。在这里，我们介绍了一例65岁男性空肠中出现的MC。该患者出现穿孔性腹膜炎伴肝转移的特征，没有已知的诱发因素，例如炎症性肠病和乳糜泻。对该肿瘤的结肠对应物进行的研究显示了微卫星不稳定性（MSI）和B型Raf激酶（BRAF）突变；然而，很少有例外。此外，已知这种癌症亚型比其他组织学亚型具有更好的预后。
