关键词: Adipose tissue neoplasms Lipoblastoma-like Mesenchymal neoplasms Neoplasia mesenquimal Neoplasia vulvar Neoplasias adiposas Tipo lipoblastoma Vulvar neoplasms

Mesh : Adult Diagnosis, Differential Female Humans Lipoblastoma / diagnosis pathology Neoplasms, Adipose Tissue / pathology Soft Tissue Neoplasms / pathology Vulvar Neoplasms / diagnosis pathology

来  源:   DOI:10.1016/j.patol.2019.10.001

Abstract:
Lipoblastoma-like tumor of the vulva (LBLTV) was first described as a benign mesenchymal neoplasia; it was not recognized as a separate diagnosis in the 2013 WHO classification of soft-tissue tumors. To date, only 19 cases have been reported. LBLTV differential diagnosis includes other tumors of the vulvoperineal region and tumors with adipocytic differentiation, most of which are benign and thus a misdiagnosis has few clinical consequences. However, LBLTV may also mimic some aggressive lipomatous neoplasms. We describe a case of LBLTV in a 28 year-old woman and review the literature.
摘要:
外阴脂肪母细胞瘤样肿瘤(LBLTV)最初被描述为良性间叶瘤;在2013年WHO软组织肿瘤分类中,它没有被视为单独的诊断。迄今为止,仅报告了19例。LBLTV鉴别诊断包括外阴会阴区的其他肿瘤和具有脂肪细胞分化的肿瘤,其中大多数是良性的,因此误诊几乎没有临床后果。然而,LBLTV还可以模拟一些侵袭性脂肪瘤。我们描述了一名28岁女性的LBLTV病例,并回顾了文献。
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