Abstract：
Existed classifications of congenital proximal radioulnar synostosis (PRUS) mainly focus on osseous changes and do not cover all types of congenital PRUS, ignoring the role and developing status of the supinator. This study aims to explore the correlation between supinator development and radiographic deformity of congenital PRUS. Pediatric patients diagnosed with congenital PRUS in two pediatric Orthopedic centers were evaluated retrospectively. MRI and radiographic images of their bilateral forearms (including normal ones) were collected. The area of supinator, extensor carpi radialis longus (ECRL), extensor carpi radialis brevis (ECRB), brachioradialis (BRAR) muscle and extensor indicis (EI) muscle were measured on each forearm. The ratios of these muscles were calculated and regarded as an indicator of the developing status of supinator muscle. Twenty-seven congenital PRUS forearms of 16 patients (average 3.45 years) were included. A new MRI & X-ray classification system was proposed to cover all types of radiographic deformity and provide a comprehensive description of supinator development. This study revealed the relation between MRI measured supinator volume and radiographic deformity of congenital PRUS. Supinator muscles were observed in all congenital PRUS cases. A novel classification was proposed, providing a more comprehensive understanding of congenital PRUS.
摘要：
现有的先天性近端尺桡骨滑膜（PRUS）分类主要集中在骨改变，并不涵盖所有类型的先天性PRUS。忽略了仰卧起子的作用和发展状况。本研究旨在探讨先天性PRUS的上肌发育与影像学畸形的相关性。对两个儿科骨科中心诊断为先天性PRUS的儿科患者进行了回顾性评估。收集其双侧前臂（包括正常前臂）的MRI和影像学图像。旋肌区域，桡骨腕长伸肌(ECRL)，桡侧短腕伸肌(ECRB)，在每个前臂上测量臂臂（BRAR）肌肉和指伸肌（EI）。计算这些肌肉的比率，并将其视为旋后肌发育状态的指标。包括16例（平均3.45岁）的27例先天性PRUS前臂。提出了一种新的MRI和X射线分类系统，以涵盖所有类型的放射学畸形，并提供对上肌发育的全面描述。这项研究揭示了MRI测量的旋后肌体积与先天性PRUS的影像学畸形之间的关系。在所有先天性PRUS病例中均观察到旋出肌。提出了一种新的分类，提供对先天性PRUS的更全面的了解。
