关键词: Leukocytoclastic vasculitis Waldenström hypergammaglobulinemia purpura

来  源:   DOI:10.1177/2050313X221086321   PDF(Pubmed)

Abstract:
UNASSIGNED: Hypergammaglobulinemic purpura of Waldenström is an uncommon disease, which presents mostly in women on the lower extremities. It is sometimes associated with underlying immune dysregulation. Sjögren syndrome is the most common association; however, rare occurrences of the self-resolving syndrome with lymphoma or myeloma have been reported.
UNASSIGNED: We describe an unusual and impressive presentation of hypergammaglobulinemic purpura of Waldenström in an elderly female patient with myeloma. Notably, the patient did not have any concurrent connective tissue diseases. Despite her florid presentation, her hypergammaglobulinemic purpura of Waldenström spontaneously resolved within a few days.
UNASSIGNED: Hypergammaglobulinemic purpura of Waldenström is a self-resolving but recurrent syndrome, which may be associated with autoimmune disorders or rarely myeloma. Early diagnosis of the syndrome may avoid unnecessary treatment interventions and should prompt screening for underlying diseases.
摘要:
未经证实:Waldenström的高丙种球蛋白性紫癜是一种罕见的疾病,主要表现在下肢的女性身上。它有时与潜在的免疫失调有关。干燥综合征是最常见的关联;然而,据报道,罕见的淋巴瘤或骨髓瘤自我解决综合征的发生。
UNASSIGNED:我们描述了一位患有骨髓瘤的老年女性患者的Waldenström高丙种球蛋白性紫癜的一个不寻常且令人印象深刻的表现。值得注意的是,患者没有任何并发结缔组织疾病。尽管她华丽的演讲,她的Waldenström高丙种球蛋白性紫癜在几天内自发缓解。
未经授权:Waldenström的高丙种球蛋白性紫癜是一种自我解决但反复发作的综合征,可能与自身免疫性疾病或罕见的骨髓瘤有关。该综合征的早期诊断可以避免不必要的治疗干预措施,并应及时筛查潜在疾病。
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