Abstract：
Endolymphatic sac tumors are rare benign neoplasms with locally aggressive behavior located in the posterior petrous ridge of the temporal bone. They cause sensorineural hearing loss and may develop vestibular damage. A 24-year-old male patient arrived at our office with a history of acute vertiginous syndrome, left hearing loss, and tinnitus 1-year ago. His chief complaint was an increase in auditory symptoms. A CT scan and MRI showed an endolymphatic sac tumor. Complete resection of the lesion was achieved by a transmastoid and translabyrinthine approach. Low-grade adenocarcinoma was confirmed by histopathology. The patient remained without clinical vestibular symptoms. However, a small residual tumor was addressed by gamma-ray radiosurgery. Postoperative deep left sensorineural hearing loss was identified, without any vestibular sequelae. Radiologic imaging is the most useful tool for this diagnosis. Endolymphatic sac tumors should be in the differential diagnosis of recalcitrant audio-vestibular symptoms. Complete surgical resection is the most appropriate management.
摘要：
内淋巴囊肿瘤是罕见的良性肿瘤，具有位于颞骨后岩脊的局部攻击行为。它们会导致感觉神经性听力损失，并可能导致前庭损伤。一名24岁的男性患者来到我们的办公室，有急性眩晕综合征的病史，左听力损失,还有1年前的耳鸣.他的主要主诉是听觉症状增加。CT扫描和MRI显示内淋巴囊肿瘤。通过经乳突和经迷路入路可完全切除病变。组织病理学证实为低度腺癌。患者没有临床前庭症状。然而,通过伽马射线放射外科治疗了一个小的残留肿瘤.术后深左感音神经性听力损失被确认,没有前庭后遗症.放射学成像是这种诊断最有用的工具。内淋巴囊肿瘤应在顽固性音频前庭症状的鉴别诊断中。完整的手术切除是最合适的管理。
