PDF(Pubmed)
Abstract：
OBJECTIVE: To report a rare case of orbital angioleiomyoma (ALM) and its management.
METHODS: A 22-year-old woman presented with slowly progressive painless axial proptosis. Computed tomography and magnetic resonance imaging demonstrated a well-defined intraconal mass that was isointense in T1 and hyperintense in T2 weighted images, heterogeneously enhanced by gadolinium.
RESULTS: The tumor, despite having significant adhesions to surrounding tissues and noticeable hemorrhage, was excised completely via the lateral orbitotomy approach. Histopathologic analysis of the specimen was consistent with an orbital ALM. The patient recovered from the operation uneventfully.
CONCLUSIONS: ALM must be considered in the differential diagnoses of orbital tumors.
METHODS: A 22-year-old woman presented with slowly progressive painless axial proptosis. Computed tomography and magnetic resonance imaging demonstrated a well-defined intraconal mass that was isointense in T1 and hyperintense in T2 weighted images, heterogeneously enhanced by gadolinium.
RESULTS: The tumor, despite having significant adhesions to surrounding tissues and noticeable hemorrhage, was excised completely via the lateral orbitotomy approach. Histopathologic analysis of the specimen was consistent with an orbital ALM. The patient recovered from the operation uneventfully.
CONCLUSIONS: ALM must be considered in the differential diagnoses of orbital tumors.
摘要：
目的：报告1例罕见的眼眶血管平滑肌瘤（ALM）及其治疗。
方法：一名22岁女性表现为缓慢进行性无痛性轴突。计算机断层扫描和磁共振成像显示出明确的内部肿块，在T1中具有等强度，在T2加权图像中具有高强度，被钆异质增强。
结果：肿瘤，尽管与周围组织有明显的粘连和明显的出血，通过外侧眼眶切开术完全切除。标本的组织病理学分析与眼眶ALM一致。病人从手术中顺利康复。
结论：眼眶肿瘤的鉴别诊断必须考虑ALM。
方法：一名22岁女性表现为缓慢进行性无痛性轴突。计算机断层扫描和磁共振成像显示出明确的内部肿块，在T1中具有等强度，在T2加权图像中具有高强度，被钆异质增强。
结果：肿瘤，尽管与周围组织有明显的粘连和明显的出血，通过外侧眼眶切开术完全切除。标本的组织病理学分析与眼眶ALM一致。病人从手术中顺利康复。
结论：眼眶肿瘤的鉴别诊断必须考虑ALM。
