女性儿童的膀胱和尿道重复以及膀胱外翻板伴有脐膨出。Bladder and urethral duplication and a bladder exstrophy plate with omphalocele in a female child.-医云文献数字医云科研云海量医学决策数据服务

Abstract：

The Exstrophy - Epispadias Complex (EEC) is a spectrum of rare congenital malformations involving the urinary, genital and musculoskeletal systems. We present an atypical or variant case of EEC in which a bladder plate is found involving a small omphalocele, separated pubic bones and bladder and urethral duplication. The treatment had a favorable outcome, with bladder control and the child voiding normally. Perhaps the best accepted embryonic theory to explain exstrophy and its variants should be reviewed as it fails to satisfactorily explain the alterations we found.

摘要：

Exstrophy-Epispadias复合体（EEC）是一系列罕见的涉及泌尿的先天性畸形，生殖器和肌肉骨骼系统。我们介绍了EEC的非典型或变体病例，其中发现膀胱板涉及小的脐膨出，耻骨分离，膀胱和尿道重复。治疗结果良好,膀胱控制和儿童正常排尿。也许应该审查解释exstrophy及其变体的最佳公认胚胎理论，因为它未能令人满意地解释我们发现的变化。