关键词: ectodermal dysplasia hypohidrotic syringofibroadenoma

来  源:   DOI:10.1111/ajd.13604   PDF(Sci-hub)

Abstract:
A 56-year-old woman with hypohidrotic ectodermal dysplasia presented with a 10-year history of persisting wart-like skin lesions on her feet. Biopsy revealed changes of eccrine syringofibroadenoma. These lesions are rare, with only nine case reports describing an association with ectodermal dysplasia of hidrotic type (Clouston and Schopf\'s syndrome). To our knowledge, this is the first case of eccrine syringofibroadenoma developing in the hypohidrotic/anhidrotic subtype of ectodermal dysplasia.
摘要:
一名56岁的女性,多汗性外胚层发育不良,她的脚上有10年的疣样皮肤损伤史。活检显示内分泌紫癜纤维腺瘤的变化。这些病变很罕见,只有9例病例报告描述了与多汗症型外胚层发育不良(克罗斯顿和Schopf综合征)的相关性。据我们所知,这是在外胚层发育不良的无汗症/无汗症亚型中发生的第一例内分泌-汗液-汗腺纤维腺瘤。
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