PDF(Pubmed)
Abstract：
Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option.
摘要：
先天性门静脉发育不全的患者可能由于动脉血流增加而发展为肝细胞肿瘤。这些肿瘤可能是良性的（FNH，腺瘤）或恶性（肝母细胞瘤，HCC）。可以建议肝切除术，术前动脉栓塞可以减少术中失血。具有PV重建的肝移植也是一种选择。
