%0 Case Reports
%T Stepwise management of hepatocellular carcinoma associated with Abernethy syndrome.
%A Christou N
%A Dib N
%A Chuffart E
%A Taibi A
%A Durand-Fontanier S
%A Valleix D
%A Mathonnet M
%J Clin Case Rep
%V 6
%N 5
%D May 2018
%M 29744090
暂无%R 10.1002/ccr3.1384
%X Patients with congenital agenesis of the portal vein may develop hepatocellular tumors due to enhanced arterial blood flow. These tumors may be benign (FNH, adenomas) or malignant (hepatoblastoma, HCC). Liver resection can be proposed, and preoperative arterial embolization may decrease blood loss during surgery. Liver transplantation with PV reconstruction is also an option.