Mesh ： Blood Glucose Carbohydrate Metabolism, Inborn Errors / blood drug therapy surgery urine Child, Preschool Female Humans Isotonic Solutions / therapeutic use Ketone Bodies / urine Monosaccharide Transport Proteins / blood deficiency urine Perioperative Care Perioperative Period Sodium Bicarbonate / therapeutic use

来  源：   DOI：10.1213/XAA.0000000000000727   PDF(Sci-hub)

Abstract：
Glucose transporter type 1 deficiency syndrome (GLUT1DS) causes central nervous system dysfunction including intractable epilepsy caused by impaired glucose transport to the brain. To prevent convulsions and maintain an energy source for the brain in patients with GLUT1DS, the maintenance of adequate ketone body concentrations, compensation of metabolic acidosis, and reduction of surgical stress are essential. We here report the perioperative management of a child with GLUT1DS.
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