Mesh : Antigens, Nuclear / genetics metabolism Ataxin-3 / genetics Brain / metabolism Calcium / metabolism Cell Differentiation Cell Line Cellular Reprogramming Fibroblasts / cytology metabolism Humans Induced Pluripotent Stem Cells / cytology metabolism transplantation Ionomycin / pharmacology Karyotype Machado-Joseph Disease / genetics metabolism pathology Microscopy, Fluorescence Nerve Tissue Proteins / genetics metabolism Neural Stem Cells / cytology drug effects metabolism Protein Aggregates / drug effects Repressor Proteins / genetics Synapsins / genetics metabolism Transcription Factors / genetics metabolism
来 源: DOI:10.1016/j.scr.2016.07.004 PDF(Sci-hub)