{Reference Type}: Case Reports
{Title}: Management of Patients with Vascular Ehlers-Danlos Syndrome and Acute Coronary Syndrome: a Case Report.
{Author}: Di Liberto IA;Pilato G;Caramanno G;
{Journal}: ARYA Atheroscler
{Volume}: 19
{Issue}: 1
{Year}: 2023 Jan
暂无{DOI}: 10.48305/arya.2022.11722.2343
{Abstract}: <B>BACKGROUND: </B>Ehlers-Danlos syndrome (EDS) is a hereditary collagen vascular disorder characterized by joint hypermobility, skin hyperextensibility, and tissue fragility. Vascular EDS (vEDS) is a subtype of EDS which is characterized by vascular fragility.<BR><B>METHODS: </B>This is a case report of a young man with vEDS hospitalized for myocardial infarction. He was presented with a coronary dissection and developed aortic dissection, coronary rupture, and cardiac tamponade until death.<BR><B>CONCLUSIONS: </B>This case report highlights how patients with vEDS and acute coronary syndrome show a higher risk of vascular complications compared with other patients, and their admission to the institution with a cardiac surgery room could be helpful and safe for better management of the complications. Non-invasive methods could be useful to exclude other vascular diseases, before the emergency coronary intervention.