{Reference Type}: Case Reports
{Title}: Benign to Malignant Hepatic Lesion Transformation in Abernethy Malformation.
{Author}: Tom CK;Ter-Oganesyan R;Shefali C;Kaur N;Pace JL;Rastegarpour A;Genyk Y;Kahn JA;
{Journal}: ACG Case Rep J
{Volume}: 11
{Issue}: 4
{Year}: 2024 Apr
暂无{DOI}: 10.14309/crj.0000000000001307
{Abstract}: Abernethy malformation or congenital extrahepatic portosystemic shunt is an extremely rare condition whereby the portomesenteric blood drains into a systemic vein and bypasses the liver through a complete or partial shunt. Severe complications include hyperammonemia and encephalopathy, benign and malignant liver tumors, and hepatopulmonary syndrome. We describe a case where a female adult diagnosed with congenital extrahepatic portosystemic shunt subsequently developed focal nodular hyperplasia and then hepatocellular carcinoma.