{Reference Type}: Journal Article
{Title}: Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.
{Author}: Federici S;Cinicola BL;La Torre F;Castagnoli R;Lougaris V;Giardino G;Volpi S;Caorsi R;Leonardi L;Corrente S;Soresina A;Cancrini C;Insalaco A;Gattorno M;De Benedetti F;Marseglia GL;Del Giudice MM;Cardinale F;
{Journal}: Front Pediatr
{Volume}: 11
{Issue}: 0
{Year}: 2023
{Factor}: 3.569
{DOI}: 10.3389/fped.2023.1258301
{Abstract}: Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.