{Reference Type}: Case Reports
{Title}: A distinct case of an 8-year-old female with cyclic neutropenia presenting with C. septicum abdominal sepsis and myonecrosis requiring a bowel resection and leg fasciotomy.
{Author}: Anzinger H;Cadili L;Li A;Barclay A;Hayashi AH;
{Journal}: J Surg Case Rep
{Volume}: 2023
{Issue}: 9
{Year}: 2023 Sep
暂无{DOI}: 10.1093/jscr/rjad512
{Abstract}: Clostridium septicum is a very rare cause of severe spontaneous pediatric enterocolitis and is often associated with underlying malignancy or immunocompromise. Likewise, cyclic neutropenia is a rare congenital immunodeficiency that is characterized by cyclical periods of neutropenia, often with more severe symptoms in the pediatric population. Here, we present a unique case of spontaneous C. septicum enterocolitis, sepsis, and myonecrosis in a child with undiagnosed cyclic neutropenia. Early recognition of pediatric sepsis, frequent reevaluation and identification of rapidly progressive infection, and early surgical intervention are critical for the effective management of a rare and severe infection.