{Reference Type}: Case Reports
{Title}: Malignant Pigmented Epithelioid Angiomyolipoma of the Kidney in a Child with Tuberous Sclerosis Complex.
{Author}: Phan TDA;To NT;Pham DTN;
{Journal}: Fetal Pediatr Pathol
{Volume}: 42
{Issue}: 2
{Year}: Apr 2023
{Factor}: 1.412
{DOI}: 10.1080/15513815.2022.2088911
{Abstract}: <B>BACKGROUND: </B>Pigmented epithelioid angiomyolipoma is a variant of epithelioid angiomyolipoma (EAML) that has not previously been described in children with tuberous sclerosis.<BR><B>METHODS: </B>A 15-year-old boy with tuberous sclerosis had a rapidly enlarging renal mass associated with a left lung nodule. Microscopically it was a pigmented EAML, confirmed by immunohistochemistry.<BR><B>CONCLUSIONS: </B>The pigmented variant of EAML can arise and metastasize from the kidney of a teenager with tuberous sclerosis.