{Reference Type}: Journal Article
{Title}: Hemangioma - A pointer to Abernethy syndrome?
{Author}: Kothari SS;
{Journal}: Ann Pediatr Cardiol
{Volume}: 13
{Issue}: 3
{Year}: Jul-Sep 2020
暂无{DOI}: 10.4103/apc.APC_91_20
{Abstract}: Diffuse pulmonary arteriovenous malformations or pulmonary arterial hypertension (PAH) may result from congenital portosystemic venous shunts. Hemangioma as a physical sign of congenital portosystemic shunts (like Abernethy syndrome) has not been described. I report two children (one with severe cyanosis from pulmonary arteriovenous malformations and the other with severe PAH) with cutaneous hemangioma and Abernethy syndrome. Hemangioma may be a clinical pointer to portosystemic shunts even in the absence of obvious liver disease.