{Reference Type}: Case Reports {Title}: A rare case of accessory maxilla: a case report and literature review of Tessier no. 7 clefts. {Author}: Sun M;Lv N;Xiao Y;Li J;Guan G; {Journal}: J Int Med Res {Volume}: 48 {Issue}: 5 {Year}: May 2020 {Factor}: 1.573 {DOI}: 10.1177/0300060520925680 {Abstract}: Bilateral Tessier no. 7 clefts are rarely reported in the literature. Here, we describe the presence of accessory maxilla with supernumerary teeth in a patient who exhibited bilateral Tessier no. 7 clefts; the diagnosis was established based on the patient's history, clinical presentation, and computed tomography images. A review of the available literature revealed 24 patients with Tessier no. 7 clefts from 2000 to 2020, including our patient. The most common clinical manifestation in patients with Tessier no. 7 clefts comprises bilateral facial clefts. Additionally, Tessier no. 7 clefts are more frequently found in boys or men, rather than in girls or women. The presence of an accessory maxilla with supernumerary teeth in a patient with bilateral Tessier no. 7 clefts is extremely rare. Early detection of craniofacial abnormalities is important, because it may influence patient prognosis and management.