{Reference Type}: Journal Article
{Title}: Unsuccessful tracheal intubation in a patient with Kniest dysplasia undergoing repeated general anesthesia: a case report.
{Author}: Hasegawa-Moriyama M;Iwasaki T;Mukaihara K;Masuda M;Kanmura Y;
{Journal}: JA Clin Rep
{Volume}: 4
{Issue}: 1
{Year}: May 2018 18
暂无{DOI}: 10.1186/s40981-018-0178-x
{Abstract}: <B>BACKGROUND: </B>Kniest dysplasia is a type of chondrodysplasia characterized by severe craniofacial abnormalities including tracheomalacia, midface hypoplasia, and cleft palate.<BR><B>METHODS: </B>We previously described a 6-year-old girl with Kniest dysplasia, in whom glottic edema rapidly developed after tracheal intubation. At the age of 13 years, a reoperation was scheduled to correct talipes equinovarus but was subsequently canceled due to failure of tracheal intubation and subsequent glottic edema. Airway evaluation by endoscopy and computed tomography 1 month later revealed severe laryngeal narrowing. Therefore, the second anesthesia was maintained with spinal anesthesia combined with sciatic nerve block without tracheal intubation.<BR><B>CONCLUSIONS: </B>Careful perioperative airway evaluation is required in patients with Kniest dysplasia, and alternative strategies for airway management other than tracheal intubation should be considered.