{Reference Type}: Case Reports
{Title}: A rare case of association between Budd-Chiari syndrome and sea-blue histiocytosis.
{Author}: Hu F;Zhang Y;Yi Z;
{Journal}: Niger J Clin Pract
{Volume}: 22
{Issue}: 11
{Year}: Nov 2019
暂无{DOI}: 10.4103/njcp.njcp_43_19
{Abstract}: Budd-Chiari syndrome (BCS) is a rare disease characterized by obstruction of hepatic venous outflow tract with diversified etiologies. Sea-blue histiocytosis (SBH) is a kind of storage diseases defined by the deposition of abundant sea-blue histiocytes in various organs and can lead to hepatosplenomegaly, cirrhosis, or even liver failure. The association between BCS and SBH has never been reported before. Here, we report a patient with BCS presenting with hepatosplenomegaly, portal hypertension, and pancytopenia who was later confirmed to also have SBH.