{Reference Type}: Case Reports
{Title}: IgG4-related small-sized occlusive vasculitis in Mikulicz's disease.
{Author}: Ikeoka K;Watanabe T;Ohkawa T;Tsuzuki T;Ikeda Y;Takeda M;Hoshida S;
{Journal}: J Vasc Surg Cases Innov Tech
{Volume}: 5
{Issue}: 3
{Year}: Sep 2019
暂无{DOI}: 10.1016/j.jvscit.2019.03.019
{Abstract}: Mikulicz's disease is one of the IgG4-related diseases (IgG4-RDs) that involves the cardiovascular system; however, small-sized vasculitis is rare in IgG4-related diseases. A 64-year-old man presented with distal occlusive disease and developed left cerebrovascular infarction with occlusion of the middle cerebral artery and diseased temporal artery branches. He underwent superficial temporal artery-middle cerebral artery anastomosis surgery. Histology of the temporal artery biopsy showed smooth muscle cell proliferation with many IgG4-positive plasma cells. He then developed salivary gland inflammation, and Mikulicz's disease was diagnosed. Small-sized occlusive vasculitis was observed in this IgG4-RD. Low-dose corticosteroid therapy is effective in preventing progressive occlusive disease.