{Reference Type}: Case Reports
{Title}: Anesthesia in a pediatric patient with ROHADD syndrome.
{Author}: Esparza Isasa E;Palomero Rodríguez MA;Acebedo Bambaren I;Medrano Viñas C;Gil Mayo D;Domínguez Pérez F;Pestaña Lagunas D;
{Journal}: Rev Esp Anestesiol Reanim (Engl Ed)
{Volume}: 65
{Issue}: 9
{Year}: Nov 2018
暂无{DOI}: 10.1016/j.redar.2018.03.005
{Abstract}: Rapid-onset obesity with hypothalamic dysfunction, hypoventilation, and autonomic dysregulation (ROHHAD) syndrome is a rare entity that is characterised by its onset in healthy children at 2-4 years of age. It is a complex syndrome that includes, among other symptoms, rapid weight gain with hyperphagia, hypothalamic dysfunction, central hypoventilation, and autonomic dysregulation. The case is presented of a 10-year-old boy with a diagnosis of ROHHAD syndrome undergoing insertion of a port-a-cath under general anaesthesia, who developed complications during the anaesthetic procedure related to his illness. The peri-operative management of these patients represents a challenge for the anaesthetist, given the involvement of multiple systems and the frequent respiratory comorbidities associated with them. A summary is presented of some of the implications and anaesthetic considerations that must be taken into account in the management of these patients.