{Reference Type}: Journal Article
{Title}: Systemic Sclerosis Sine Scleroderma in Mexican Patients. Case Reports.
{Author}: Vera-Lastra O;Sauceda-Casas CA;Domínguez MDPC;Alvarez SAM;Sepulceda-Delgado J;
{Journal}: Reumatol Clin (Engl Ed)
{Volume}: 14
{Issue}: 4
{Year}: Jul 2018 0
暂无{DOI}: 10.1016/j.reuma.2016.11.004
{Abstract}: Systemic sclerosis sine scleroderma (ssSSc) is a form of systemic sclerosis that is characterized by Raynaud's phenomenon (RP), visceral involvement without thickening of skin and anticentromere antibodies (ACA). We studied 10 ssSsc patients with a prevalence of 2%. The clinical signs were: RP 9/10, esophageal manifestations 8/10, pulmonary arterial hypertension 4/10, interstitial lung disease 4/10, cardiac signs 3/10 and ACA 8/10.<BR><B>CONCLUSIONS: </B>In patients with RP, esophageal dysmotility, interstitial lung disease and pulmonary arterial hypertension should be tested for ACA in order to establish a prompt diagnosis and treatment of ssSSc.