{Reference Type}: Case Reports
{Title}: Unilateral autosomal dominant polycystic kidney disease with contralateral renal agenesis: a case report.
{Author}: Jeong GH;Park BS;Jeong TK;Ma SK;Yeum CH;Kim SW;Kim NH;Choi KC;
{Journal}: J Korean Med Sci
{Volume}: 18
{Issue}: 2
{Year}: Apr 2003
{Factor}: 5.354
{DOI}: 10.3346/jkms.2003.18.2.284
{Abstract}: Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary renal disease. There are some reports in the literature concerning unilateral ADPKD. However, in adults, only a few cases of unilateral ADPKD with agenesis of contralateral kidney have been reported. We present a case of unilateral ADPKD with agenesis of contralateral kidney in a 66-yr-old man. Radiographic images showed the enlarged right kidney with multiple variable-sized cysts and the absence of the left kidney. The diagnosis of ADPKD was confirmed by the family screening. The patient received maintenance hemodialysis for endstage renal disease. We report a case of unilateral ADPKD associated with contralateral renal agenesis in a 66-yr-old male patient with a literature review.