%0 Case Reports %T IgG4 porta-hepatis pseudotumor mimicking a hilar cholangiocarcinoma. %A Wasbotten RK %A Kaur S %A Davis RM %A Nasrullah A %J Radiol Case Rep %V 19 %N 10 %D 2024 Oct %M 39114863 暂无%R 10.1016/j.radcr.2024.06.053 %X A 60-year-old female with a BRCA2 mutation and a history of breast cancer presented with diffuse abdominal pain and elevated liver enzymes. Imaging revealed a porta-hepatis mass, prompting consideration of hilar cholangiocarcinoma or breast cancer metastasis. Further investigation including biopsy and 18F-fluorodeoxyglucose positron emission tomography/computed tomography findings were inconsistent with malignancy, leading to investigation of non-neoplastic causes. Elevated IgG4 levels suggested IgG4-related disease, a mass-forming fibroinflammatory condition. This case demonstrates IgG4-related disease exclusively impacting the portal vein and underscores the importance of considering IgG4-related disease in the differential diagnosis of hepatic masses.