%0 Journal Article %T A Man with Primary Hyperchylomicronemia with Triglyceride Levels Exceeding 11,000 mg/dL was Well Controlled by Pemafibrate Combined with Dietary Therapy: A Case Report. %A Ueda H %A Mineo R %A Sugiyama T %A Koseki M %A Itoh Y %A Iwamoto R %A Tamba S %A Yamamoto K %A Yamada Y %A Hiraoka H %A Matsuzawa Y %J Intern Med %V 0 %N 0 %D 2024 Jul 25 %M 39048362 %F 1.282 %R 10.2169/internalmedicine.3946-24 %X A 50-year-old man with a triglyceride (TG) level of 11,397 mg/dL was admitted to our hospital. He consumed a high-fat and high-carbohydrate diet as well as more than 100 g of alcohol per day. He had type 2 diabetes and obesity and had previously suffered from severe acute pancreatitis twice. A genetic analysis revealed compound heterozygous mutations in APOA5 (c.56C>G and c.553G>T). In addition to low-fat meals and alcohol cessation, administration of pemafibrate lowered his triglyceride levels to <150 mg/dL.