%0 Journal Article %T Extraskeletal Ewing Sarcoma Disguised as a Vascular Malformation. %A Giri SK %A Rajpoot A %A Suba S %J J Hand Surg Asian Pac Vol %V 29 %N 4 %D 2024 Aug 12 %M 39005180 暂无%R 10.1142/S242483552472010X %X Extraskeletal Ewing sarcoma (EES) is a rare entity, accounting for only 3% of lesions encountered in upper extremity. We present two paediatric patients, who were initially diagnosed with a vascular malformation based on clinical assessment and imaging. Final histopathology revealed Ewing sarcoma of soft tissue origin, confirmed by immunohistochemical analysis. Hand surgeons, who are routinely approached for a myriad of hand pathologies, should be wary and consider EES as a differential when treating such lesions. A multidisciplinary approach with an appropriate treatment algorithm can help in a speedy diagnosis, improving the long-term prognosis of the disease. Level of Evidence: Level V (Therapeutic).