%0 Case Reports
%T Extraskeletal myxoid chondrosarcoma metastasis to a Meckel's diverticulum adenocarcinoma.
%A Gama JM
%A Oliveira RC
%A Fonseca R
%A Cipriano MA
%A Casanova J
%J Rev Esp Patol
%V 57
%N 2
%D 2024 Apr-Jun
%M 38599736
暂无%R 10.1016/j.patol.2023.12.002
%X Extraskeletal myxoid chondrosarcoma is a rare soft tissue tumour with a high local and distant metastasis rate and limited response to chemotherapy. Meckel's diverticulum is the most frequent congenital anomaly, and it is associated with a considerable risk of malignant transformation. In this case report, we describe a 50-year-old female patient with a history of extraskeletal myxoid chondrosarcoma of the lower limb and metastasis to the forearm who went to the emergency department with abdominal pain. The investigations revealed a caecal volvulus. A lesion in the middle third of the ileum was incidentally discovered and removed during surgery. Pathology examination revealed a Meckel's diverticulum adenocarcinoma, with metastasis of extraskeletal myxoid chondrosarcoma. Resection was complete; however, the patient had diffuse metastatic pulmonary disease and died eight months later due to disease progression. This mechanism of tumour-to-tumour metastasis is described in other locations, but, regarding the Meckel's diverticulum, this is a unique situation, previously unreported in the literature.