%0 Case Reports
%T Ophthalmic Manifestations as First Presenting Sign of Evans Syndrome.
%A Mazharuddin AA
%A Rehmani A
%A Puthenparambil L
%A Alappatt JJ
%A Lee WH
%J J Vitreoretin Dis
%V 6
%N 6
%D Nov-Dec 2022
%M 37009543
暂无%R 10.1177/24741264211062931
%X <B>UNASSIGNED: </B>This work reports a case of Evans syndrome first presenting with ophthalmic signs.<BR><B>UNASSIGNED: </B>A 27-year-old previously healthy man presented with headaches and bilateral blurred vision for 2 weeks. The visual acuity was 20/30-1 and 20/60-2 in the right eye and left eye, respectively. A fundus examination revealed Roth spots, diffuse multilayer retinal hemorrhages in the macula and periphery, and tortuous vessels in both eyes. Optical coherence tomography showed a disrupted foveal contour from intraretinal fluid and hemorrhage in both eyes. Fluorescein angiography demonstrated dilated and tortuous vessels with scattered blocking defects from hemorrhages.<BR><B>UNASSIGNED: </B>A workup revealed warm hemolytic anemia with severe thrombocytopenia consistent with the diagnosis of Evans syndrome.<BR><B>UNASSIGNED: </B>Evans syndrome is a rare blood dyscrasia that can first present as subacute vision loss and should be added to the differential of diffuse bilateral retinal hemorrhages spanning a multitude of retinal layers.