%0 Case Reports %T Palmoplantar keratoderma: An unusual manifestation of hypohydrotic ectodermic dysplasia. %A Abdelli W %A Souissi A %A Alaoui F %A Sassi W %A Chelly I %A Haouat S %A Mokni M %A Abdelli W %A Souissi A %A Alaoui F %A Sassi W %A Chelly I %A Haouat S %A Mokni M %J Clin Case Rep %V 10 %N 3 %D Mar 2022 %M 35310322 暂无%R 10.1002/ccr3.5577 %X Rapp-Hodgkin syndrome (RHS) is a rare condition that is characterized by ectodermal dysplasia and palatal abnormalities. Palmoplantar keratoderma (PPK) is an unusual manifestation of hidrotic ED. Ulcerations on the palms are also not common in RHS. We describe a 15-year-old boy who has RHS associated with PPK.