%0 Journal Article %T International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes. %A Michelena HI %A Della Corte A %A Evangelista A %A Maleszewski JJ %A Edwards WD %A Roman MJ %A Devereux RB %A Fernández B %A Asch FM %A Barker AJ %A Sierra-Galan LM %A De Kerchove L %A Fernandes SM %A Fedak PWM %A Girdauskas E %A Delgado V %A Abbara S %A Lansac E %A Prakash SK %A Bissell MM %A Popescu BA %A Hope MD %A Sitges M %A Thourani VH %A Pibarot P %A Chandrasekaran K %A Lancellotti P %A Borger MA %A Forrest JK %A Webb J %A Milewicz DM %A Makkar R %A Leon MB %A Sanders SP %A Markl M %A Ferrari VA %A Roberts WC %A Song JK %A Blanke P %A White CS %A Siu S %A Svensson LG %A Braverman AC %A Bavaria J %A Sundt TM %A El Khoury G %A De Paulis R %A Enriquez-Sarano M %A Bax JJ %A Otto CM %A Schäfers HJ %A %J Eur J Cardiothorac Surg %V 60 %N 3 %D 09 2021 11 %M 34293102 %F 4.534 %R 10.1093/ejcts/ezab038 %X This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.