%0 Case Reports
%T [A case of congenital hepatic fibrosis diagnosed and treated by transjugular intrahepatic portosystemic shunt].
%A Wang J
%A Shu J
%A Wu F
%A Song ZT
%A Gan HY
%A Yu J
%A Zheng D
%J Zhonghua Gan Zang Bing Za Zhi
%V 29
%N 4
%D Apr 2021 20
%M 33979966
暂无%R 10.3760/cma.j.cn501113-20190527-00190
%X 先天性肝纤维化（CHF）是一种罕见的与胆管板畸形相关的肝内胆管遗传发育障碍疾病，无特异性临床表现，易误诊或漏诊。现报道1例误诊为肝硬化并发食管胃底静脉曲张破裂出血患者在行经颈静脉肝内门体分流术（TIPS）治疗时发现，最后经病理学检查确诊为CHF患者的临床资料，以期提高CHF的诊治水平。.