%0 Journal Article %T Nystagmus in patients with lateral semicircular canal dysplasia. %A Choi B %A Lee DH %A Shin JE %A Kim CH %J Acta Otolaryngol %V 140 %N 12 %D Dec 2020 %M 32808842 %F 1.698 %R 10.1080/00016489.2020.1804615 %X BACKGROUND: Dizziness is not a common symptom in the lateral semicircular canal (LSCC) dysplasia, and nystagmus findings has been rarely described in LSCC dysplasia.
OBJECTIVE: To investigate the characteristics of spontaneous and positional nystagmus in patients with LSCC dysplasia.
METHODS: Patterns of spontaneous and positional nystagmus of twelve patients with LSCC dysplasia, who visited our clinic with a chief complaint of dizziness, were investigated.
RESULTS: LSCC dysplasia was observed unilaterally in 4, and bilaterally in 8 patients. Non-rotatory dizziness with various onset times was the most common description of dizziness, and unilateral caloric weakness was observed in 82% of patients. Direction-fixed nystagmus, in which the direction of spontaneous nystagmus was same with that of positional nystagmus, was observed in 9 patients, and direction-changing positional nystagmus, in which the direction of nystagmus was changed from that of spontaneous nystagmus by positioning maneuvers, was observed in 3 patients, of whom down-beating or direction-changing spontaneous nystagmus was observed in one patient each.
CONCLUSIONS: While direction-fixed horizontal nystagmus is the most commonly observed type of nystagmus in LSCC dysplasia, atypical spontaneous nystagmus, such as down-beating nystagmus or direction-changing spontaneous nystagmus, may be observed in patients with bilateral LSCC dysplasia.