%0 Case Reports
%T A rare case of association between Budd-Chiari syndrome and sea-blue histiocytosis.
%A Hu F
%A Zhang Y
%A Yi Z
%J Niger J Clin Pract
%V 22
%N 11
%D Nov 2019
%M 31719286
暂无%R 10.4103/njcp.njcp_43_19
%X Budd-Chiari syndrome (BCS) is a rare disease characterized by obstruction of hepatic venous outflow tract with diversified etiologies. Sea-blue histiocytosis (SBH) is a kind of storage diseases defined by the deposition of abundant sea-blue histiocytes in various organs and can lead to hepatosplenomegaly, cirrhosis, or even liver failure. The association between BCS and SBH has never been reported before. Here, we report a patient with BCS presenting with hepatosplenomegaly, portal hypertension, and pancytopenia who was later confirmed to also have SBH.