%0 Case Reports
%T Carcinoid Syndrome-Induced Scleroderma-Like Disease.
%A Koch K
%A Grayson W
%J Dermatopathology (Basel)
%V 6
%N 2
%D Apr-Jun 2019
%M 31700850
暂无%R 10.1159/000496388
%X Scleroderma is a rare complication of carcinoid syndrome and is usually encountered in the setting of a metastatic primary neuroendocrine tumour of the distal ileum. Associated endocardial fibrosis is a frequent finding and the condition carries a poor prognosis. We report a case of scleroderma occurring in a 72-year-old female with metastatic neuroendocrine carcinoma and associated pericardial fibrosis. The use of an alternative nomenclature such as "scleroderma-like" or "sclerodermoid" disease is proposed in order to emphasise its distinction from true idiopathic scleroderma, despite the histopathological similarities on skin biopsy.