%0 Case Reports
%T Hereditary spherocytosis with successful splenectomy in a pregnant black South African lady: a case report.
%A Elmezughi K
%A Ekpebegh C
%J Pan Afr Med J
%V 33
%N 0
%D 2019
%M 31692845
暂无%R 10.11604/pamj.2019.33.288.18873
%X Hereditary spherocytosis is a rare cause of chronic haemolytic anaemia. It is rarer in the black population with extremely few cases reported. Initial assessment of a patient with suspected disease should include documenting clinical features of chronic haemolysis and a family history. Its management in pregnancy is challenging and needs a multidisciplinary team. We report on a black South African woman with hereditary spherocytosis and massive splenomegaly presenting with severe haemolytic anaemia at 23rd week of pregnancy. She had a successful splenectomy.