%0 Case Reports
%T Cu-sil dentures: A novel approach of Papillon-Lefèvre syndrome management.
%A Tyagi S
%A Thomas AM
%A Balla V
%A Kundra R
%J J Indian Soc Pedod Prev Dent
%V 37
%N 3
%D Jul-Sep 2019
%M 31584033
暂无%R 10.4103/JISPPD.JISPPD_256_18
%X Papillon-Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1-4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.