%0 Case Reports
%T Anesthesia in a pediatric patient with ROHADD syndrome.
%A Esparza Isasa E
%A Palomero Rodríguez MA
%A Acebedo Bambaren I
%A Medrano Viñas C
%A Gil Mayo D
%A Domínguez Pérez F
%A Pestaña Lagunas D
%J Rev Esp Anestesiol Reanim (Engl Ed)
%V 65
%N 9
%D Nov 2018
%M 29728260
暂无%R 10.1016/j.redar.2018.03.005
%X Rapid-onset obesity with hypothalamic dysfunction, hypoventilation, and autonomic dysregulation (ROHHAD) syndrome is a rare entity that is characterised by its onset in healthy children at 2-4 years of age. It is a complex syndrome that includes, among other symptoms, rapid weight gain with hyperphagia, hypothalamic dysfunction, central hypoventilation, and autonomic dysregulation. The case is presented of a 10-year-old boy with a diagnosis of ROHHAD syndrome undergoing insertion of a port-a-cath under general anaesthesia, who developed complications during the anaesthetic procedure related to his illness. The peri-operative management of these patients represents a challenge for the anaesthetist, given the involvement of multiple systems and the frequent respiratory comorbidities associated with them. A summary is presented of some of the implications and anaesthetic considerations that must be taken into account in the management of these patients.