%0 Journal Article
%T Systemic Sclerosis Sine Scleroderma in Mexican Patients. Case Reports.
%A Vera-Lastra O
%A Sauceda-Casas CA
%A Domínguez MDPC
%A Alvarez SAM
%A Sepulceda-Delgado J
%J Reumatol Clin (Engl Ed)
%V 14
%N 4
%D Jul 2018 0
%M 28065485
暂无%R 10.1016/j.reuma.2016.11.004
%X Systemic sclerosis sine scleroderma (ssSSc) is a form of systemic sclerosis that is characterized by Raynaud's phenomenon (RP), visceral involvement without thickening of skin and anticentromere antibodies (ACA). We studied 10 ssSsc patients with a prevalence of 2%. The clinical signs were: RP 9/10, esophageal manifestations 8/10, pulmonary arterial hypertension 4/10, interstitial lung disease 4/10, cardiac signs 3/10 and ACA 8/10.<BR><B>CONCLUSIONS: </B>In patients with RP, esophageal dysmotility, interstitial lung disease and pulmonary arterial hypertension should be tested for ACA in order to establish a prompt diagnosis and treatment of ssSSc.