%0 Journal Article
%T Anaesthetic Management of a Patient with Pseudo-TORCH Syndrome.
%A Berk D
%A Kuş A
%A Sahin T
%A Solak M
%A Toker K
%J Balkan Med J
%V 30
%N 3
%D Sep 2013
%M 25207129
%F 3.57
%R 10.5152/balkanmedj.2013.6960
%X <B>BACKGROUND: </B>Pseudo-TORCH syndrome is a rare, chronic disorder that is characterised by dimorphic features such as microcephaly, intracranial calcification, seizures, mental retardation, hepatosplenomegaly and coagulation disorders.<BR><B>METHODS: </B>We present the anaesthetic management of a forty day-old boy with Pseudo-TORCH syndrome during magnetic resonance imaging. Microcephaly, growth failure, high palate and bilateral rales in the lungs were detected in pre-anaesthetic physical examination. The peripheral oxygen saturation was 88-89% in room-air and was 95% in a hood with 5 L/min oxygen. We planned general anaesthesia to ensure immobility during magnetic resonance imaging. After standard monitoring, general anaesthesia was induced with 8% sevoflurane in 100% O2. After an adequate depth of anaesthesia was reached, we inserted a supraglottic airway device to avoid intubation without the use of a muscle relaxant.<BR><B>CONCLUSIONS: </B>In patients with Pseudo-TORCH syndrome, the perioperative anaesthetic risk was increased. We believe that using a supraglottic airway device to secure the airway is less invasive than intubation, and can be performed without the need of muscle relaxants.