%0 Case Reports
%T Christ-Siemens-Touraine Syndrome with Self-mutilation Habit: An Unusual Presentation.
%A Kayalvizhi G
%A Neeraja R
%J Int J Clin Pediatr Dent
%V 2
%N 1
%D Jan 2009
%M 25206102
暂无%R 10.5005/jp-journals-10005-1044
%X Ectodermal dysplasia exhibits a classic triad of hypohidrosis, hypotrichosis, and hypodontia. Self- mutilation could be due to organic or functional causes. The occurrence of selfmutilation with functional cause represents a diagnostic challenge to practitioners. In most of the instances dentists are the first to recognize patient with ectodermal dysplasia as they report primarily with a complaint of missing teeth. The most common type is hypohidrotic ectodermal dysplasia (Christ-Siemens-Touraine syndrome). A thorough knowledge of this disease with multidisciplinary approach aids in successful outcome of the treatment. This is an unusual case report of Christ-Siemens-Touraine syndrome with selfmutilation.